Intra-abdominal desmoplastic small round cell tumor: Presentation of four cases and review of the literature
نویسندگان
چکیده
منابع مشابه
Intra-abdominal desmoplastic small round cell tumor
BACKGROUND The desmoplastic small round cell tumour is a rare and aggressive intra-abdominal neoplasia, with only 200 cases reported, and a higher incidence in men and predilection for the second decade of life. Histologically characterized by the presence of small nests of undifferentiated tumour cells, wrapped in fibrous desmoplastic stroma. CLINICAL CASE A 24 year old male started with abd...
متن کاملRemoval of an intra-abdominal desmoplastic small round cell tumor by repetitive debulking surgery: A case report and literature review
In the current study, a case of recurrent desmoplastic small round cell tumor (DSRCT) is presented, which was successfully treated by repetitive debulking surgery. In May 2010, a 39-year-old male, with a history of surgical resection of intra-abdominal DSRCT, visited the Ibaraki Medical Center, Tokyo Medical University Hospital (Ami, Japan) with severe lower abdominal discomfort. Abdominal comp...
متن کاملintra-abdominal desmoplastic small round cell tumor in a 45-year-old man: a case report.
intra-abdominal desmoplastic small round cell tumor is a rare entity with a few reports worldwide. this tumor commonly occurs in children and adolescent and occurrence in adult age group is very rare. here, we describe an adult male with symptoms of intestinal obstruction due to abdominal mass, located in splenic flexure. after resection, the diagnosis of intra-abdominal desmoplastic small roun...
متن کاملIntra-Abdominal Desmoplastic Small Round Cell Tumor - Immunohistochemical and ultrastructural study -
= Abstract = We report a case of malignant intraabdominal tumor in a 14 years old Korean girl that presented with abdominal pain, distension and palpable mass. Emergency laparotomy revealed bulky peritoneal masses with numerous satellite implanting nodules. Ught microscopically the tumor was characterized by discrete islands of compact, small epithelium-like cells encased in desmoplastic stroma...
متن کاملDesmoplastic small round cell tumor: extra abdominal and abdominal presentations and the results of treatment.
BACKGROUND Desmoplastic small round cell tumor (DSRCT) is a rare malignant neoplasm of adolescent males. Current multimodality treatment prolongs life and rarely achieves cure. AIM To review the presenting features, histopathology and outcome of 18 patients with DSRCT treated at a single institution. SETTING AND DESIGN This is a retrospective observational study of patients with DSRCT who p...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Indian Journal of Medical and Paediatric Oncology
سال: 2010
ISSN: 0971-5851
DOI: 10.4103/0971-5851.68849